Cardiology in the Young

Brief Reports

Divided left atrium in association with tricuspid atresia and discordant ventriculo-arterial connections

Aygun Dindara1, William J. Brawna1 and Joseph V. De Giovannia1 c1

a1 Heart Unit, Birmingham Children's Hospital NHS Trust, Birmingham, UK

Abstract

Division of the morphologically left atrium is a rare abnormality, constituting around 0.1% of congenital heart disease. It may coexist with other cardiac abnormalities, and this association may obscure its recognition. We report an uncommon association with tricuspid atresia and discordant ventriculo-arterial connections, the latter dominating the clinical picture. Accurate diagnosis was made by transthoracic cross-sectional echocardiography, and the patient was referred to surgery without need for cardiac catheterisation.

(Accepted March 12 1997)

Correspondence:

c1 Dr J. V De Giovanni, Heart Unit, Birmingham Children's Hospital NHS Trust, Ladywood Middleway, Birmingham B16 SET, UK. Tel: 0121 450 6417; Fax: 0121 452 1791

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